英文名称
4-Methylumbelliferyl a-L-Idopyranosiduronic Acid 2-Sulfate Disodium Salt
Standards; Fluorescent Reagents; Carbohydrates and Oligosaccharides;
4-Methylumbelliferyl ?-L-Idopyranosiduronic Acid 2-Sulfate Disodium Salt is a fluorogenic substrate in the assay of ?-L-Iduronidase. A fluorimetric enzyme assay for the diagnosis of MPS II (Hunter disease).